OnlineIMD

PRPS1-related disease

  • Type
    Disease
  • External link(s)
    • IEMbase
  • Gene
    • PRPS1 / Phosphoribosyl Pyrophosphate Synthetase 1
      • Xq22.3
      • OMIM
      • GnomAD
      • Ensembl
      • HGNC
      • VMH
      • LOVD
  • Gene product
    • Phosphoribosyl pyrophosphate synthetase 1
  • Disease group(s)
    • 16.2    Disorders of purine metabolism
  • Child entries
    • Phosphoribosylpyrophosphate synthetase superactivity, severe form
    • Phosphoribosylpyrophosphate synthetase superactivity, attenuated form
    • PRPS1-related non-syndromic sensorineural deafness
    • X linked intellectual disability-limb spasticity-retinal dystrophy-arginine vasopressin deficiency
    • X-linked Charcot-Marie-Tooth disease type 5
    • Phosphoribosylpyrophosphate synthetase superactivity